TLRs (Toll-like receptors) are central components of mammalian innate immunity. Upon activation, their cytosolic TIR (Toll/interleukin-1 receptor) domains recruit the TIR-domain containing adaptor proteins MyD88 and MAL via TIR: TIR interactions. MAL works as a bridging adaptor for the association of MyD88 with TLR2 or TLR4, which in turn activates the transcription factor NF-kB to produce pro-inflammatory cytokines.
Over-activation of this signalosome may lead to chronic inflammatory conditions. Therefore, a broad-spectrum anti-inflammatory drug can be designed by targeting TLR2/4 signalling. TLR-antagonists designed against the extracellular domains of the receptors have had limited clinical outcomes. Targeting protein-protein interactions of the downstream adaptors provides an alternative approach.
The TIR-domain of MAL (MALTIR) forms spontaneous and reversible filaments in vitro. The cryo-EM structure of the MALTIR filament revealed intra- and inter-strand interfaces. Several interfacial residues are crucial for mediating TLR4 signalling. Although such structural information could be exploited for structure-based drug design, to our knowledge, no small molecule inhibitors of MALTIR have been reported.
We have recently identified several small molecule inhibitors of MALTIR filament. Among them, o-vanillin is the most potent lead molecule. To reveal the structure-activity relationships of o-vanillin-mediated MALTIR inhibition, the solution structure of the wild-type MALTIR was determined. Detailed HSQC and intermolecular-NOE analyses showed that o-vanillin preferentially targets the intrastrand interface of MALTIR filament. In particular, o-vanillin forms a Schiff base with the K210 of MALTIR, which is proximal to the intrastrand interface. Therefore, this interface of the MALTIR filament may be affected by o-vanillin induced side-chain orientation of K210, as predicted from the intermolecular-NOE-derived distance restraints. The aldehyde group of o-vanillin and its ortho-hydroxyl moiety were found to be indispensable for its inhibitory activity.
Overall, this study provides the first proof-of-principle that MALTIR function can be inhibited by small molecules, which can be advanced further as potential anti-inflammatories.